fumarase
111N-Acetylglutamate synthase deficiency — Classification and external resources N Acetylglutamic acid OMIM 237310 …
112Methylmalonyl-CoA mutase — Rendering based on PDB 2XIJ …
113Mitochondrial trifunctional protein — Schematic demonstrating mitochondrial fatty acid beta oxidation and effects of long chain 3 hydroxyacyl coenzyme A dehydrogenase deficiency, LCHAD deficiency Mitochondrial trifunctional protein is a protein which catalyzes several reactions in… …
114Cholesterol side-chain cleavage enzyme — Cytochrome P450, family 11, subfamily A, polypeptide 1 Identifiers Symbols CYP11A1; CYP11A; P450SCC External IDs …
115Enoyl-CoA hydratase — protein Name=enoyl Coenzyme A, hydratase/3 hydroxyacyl Coenzyme A dehydrogenase caption= width= HGNCid=3247 Symbol=EHHADH AltSymbols=ECHD EntrezGene=1962 OMIM=607037 RefSeq=NM 001966 UniProt=Q08426 PDB= ECnumber=4.2.1.17 Chromosome=3 Arm=q… …
116Glutathione synthetase deficiency — Classification and external resources Glutathione OMIM 266130 …
117Ornithine translocase deficiency — Classification and external resources Ornithine ICD 9 …
118Mitochondrial membrane transport protein — Mitochondrial membrane transport proteins are proteins which exist in the membranes of mitochondria and which serve to transport[1] molecules and other factors such as ions into or out of the organelles. Examples Examples of mitochondrial… …
119Steroid 11-beta-hydroxylase — Cytochrome P450, family 11, subfamily B, polypeptide 1 Identifiers Symbols CYP11B1; CPN1; CYP11B; DKFZp686B05283; FHI; FLJ36771; P450C11 External IDs …
120Dihydroorotate dehydrogenase — Dihydroorotate oxidase Identifiers EC number 1.3.3.1 CAS number 9029 03 2 …